A Rare Case of Metastatic Low-Grade Fibromyxoid Sarcoma of the Lung

Madonna E Lee1, Abu Rogers2, Hans Iwenofu3, David Liebner4, Daniel Mansour1, Ronald Figura1, Alicia Perkins1, Robert E Merritt1 and Desmond M D’Souza1*

1Division of Thoracic Surgery, The Ohio State University Wexner Medical Center, USA
2The Ohio State University, USA
3Department of Pathology, The Ohio State University Wexner Medical Center, USA
4Department of Medical Oncology, The Ohio State University Wexner Medical Center, USA

^*Correspondance to: Desmond M D’Souza 

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Abstract:

Evans tumor, also known as Low-Grade Fibromyxoid Sarcoma (LGFMS) is rare form of sarcoma,
occurring in the deep soft tissues of mostly young adult males. We describe a 36-year old man with
pulmonary LGFMS that originated from possible metastasis of a primary leg lesion. The patient
had initially been misdiagnosed with neurofibroma in their right leg. A right upper lobectomy and
mediastinal dissection were performed to remove the tumor. The tumor was completely resected,
and there has been no evidence of recurrence. LGFMS should be included as a differential for large,
benign-appearing lung masses in young adults, as complete surgical resection can be effective.

Keywords:

Low grade fibromyxoid sarcoma; Fibromyxomas; Evans tumor; Intrathoracic

Cite the Article:

Lee ME, Rogers A, Iwenofu H, Liebner D, Mansour D, Figura R, et al. A Rare Case of Metastatic Low-Grade Fibromyxoid Sarcoma of the Lung. World J Surg Surgical Res. 2020; 3: 1231..